What causes maple syrup urine disease?

Related questions

1. Can maple syrup urine disease be cured?
2. Can you die from maple syrup urine disease?
3. Why does my husband smell like maple syrup?
4. Why does my pee smell like maple syrup?
5. How is MSUD diagnosed?
6. Is foul smelling urine a sign of cancer?
7. What does it mean if my pee smells sweet?
8. What does diabetic pee smell like?
9. How long can you live with maple syrup urine disease?
10. Can galactosemia be cured?

Tags

1. #isoleucine
2. #toxic
3. #chain
4. #metabolic
5. #amino
6. #ketoacids
7. #their
8. #leucine
9. #disorder
10. #acids
11. #blood
12. #valine
13. #deficiency
14. #buildup
15. #caused
16. #branched
17. #dehydrogenase
18. #urine
19. #products
20. #complex
21. #leading
22. #bckdc
23. #alpha